Lipomyelomeningocele (LMM) is a closed type of spina bifida characterized by the infiltration of subcutaneous lipoma tissue through the lumbodorsal fascia and midline bone defect into the dura and neural tissues. It is usually associated with tethered spinal cord syndrome with clinical consequences (motor findings, urinary and fecal problems). No specific risk factor has been found in its etiology. There are 3 different types: dorsal, caudal and transitional. The most common and simplest type is the dorsal type. Although surgery in asymptomatic cases is still controversial, many cases have been reported to benefit from surgery.