Although dermal sinuses are common lesions in childhood, sinus tracts, especially those located sacral, extending to the spinal cord and causing tethered spinal cord syndrome, are rarely observed. It may occur with meningitis, tethered spinal cord syndrome, abnormal skin findings or spinal cord compression findings. Embryologically, it occurs after a closure disorder that occurs between the 3rd and 5th weeks of gestation. It occurs when the superficial ectoderm cannot be separated from the neural ectoderm. This occurs with a focal adhesion during non-separation, and the focal adhesion turns into a tube lined with epithelial cells. Thus, a small channel connecting the spinal cord and skin is formed. This is called `dermal sinus tract`. MRI is the gold standard examination in diagnosis. In dermal sinus anomaly, the most important factor affecting the outcome is performing surgery as early as possible.